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haemochromatosis

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haemochromatosis [2023/11/16 22:31] – [Clinical features of adult form] gary1haemochromatosis [2026/08/07 00:46] (current) – [Aetiology] gary1
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         * others have a milder form due to either homozygous H63D mutation or C232Y/H63D compound heterozygous mutation         * others have a milder form due to either homozygous H63D mutation or C232Y/H63D compound heterozygous mutation
       * transferrin receptor 2 (TfR2)       * transferrin receptor 2 (TfR2)
 +      * gain of function mutation in TPCN1 gene resulting in excessive activity of TPC1 ion channels may be a risk factor
 +        * TCP1 activity influences both the absorption of iron from the plasma membrane and the pH value in endosomes that release iron into the cytosol based on pH value(([[https://www.pnas.org/doi/10.1073/pnas.2602941123|2026: TPC1-dependent control of endosomal pH and transferrin uptake determines cellular iron status]]))
   *more severe juvenile onset haemochromatosis:   *more severe juvenile onset haemochromatosis:
     * mutation of genes encoding either:     * mutation of genes encoding either:
haemochromatosis.txt · Last modified: 2026/08/07 00:46 by gary1

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